Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction

Anesthetic management of a child with hemifacial microstomia and frontonasal encephalocele can be challenging due to factors such as a difficult airway, associated systemic conditions, young age, and prolonged operating time. Hereby, we outline the intraoperative management of a 3-year-old child und...

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Main Authors: Selvendiran Panneerselvam, Georgene Singh, Ananth P. Abraham, Keta Thakkar
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2024-09-01
Series:Journal of Neuroanaesthesiology and Critical Care
Subjects:
Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1791955
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author Selvendiran Panneerselvam
Georgene Singh
Ananth P. Abraham
Keta Thakkar
author_facet Selvendiran Panneerselvam
Georgene Singh
Ananth P. Abraham
Keta Thakkar
author_sort Selvendiran Panneerselvam
collection DOAJ
description Anesthetic management of a child with hemifacial microstomia and frontonasal encephalocele can be challenging due to factors such as a difficult airway, associated systemic conditions, young age, and prolonged operating time. Hereby, we outline the intraoperative management of a 3-year-old child undergoing repair of multiple defects requiring multidisciplinary involvement of neurosurgery, plastic surgery, and anesthesia team. In our case, a size 0 mask and hyper-angulated D-blade video laryngoscopy were used to prevent sac compression and facilitate intubation. Blood conservation strategies included tranexamic acid, precise fluid management, and maintenance of normothermia. Extubation was carefully planned, considering blood loss and airway edema, and performed when the child was fully awake, ensuring a stable postoperative period and successful recovery. This report emphasizes the importance of meticulous preoperative assessment, readiness for a challenging airway, efficient management of intraoperative blood loss, and the value of teamwork.
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spelling doaj-art-02d326b6f6254d1587954cba55aa384d2025-01-10T23:57:28ZengThieme Medical and Scientific Publishers Pvt. Ltd.Journal of Neuroanaesthesiology and Critical Care2348-05482348-926X2024-09-01110320320510.1055/s-0044-1791955Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia CorrectionSelvendiran Panneerselvam0Georgene Singh1https://orcid.org/0000-0003-3952-9596Ananth P. Abraham2https://orcid.org/0000-0003-2757-2108Keta Thakkar3https://orcid.org/0000-0001-8014-8619Department of Neuroanaesthesia, Christian Medical College, Vellore, Tamil Nadu, IndiaDepartment of Neuroanaesthesia, Christian Medical College, Vellore, Tamil Nadu, IndiaDepartment of Neurological Sciences, Christian Medical College, Vellore, Tamil Nadu, IndiaDepartment of Neuroanaesthesia, Christian Medical College, Vellore, Tamil Nadu, IndiaAnesthetic management of a child with hemifacial microstomia and frontonasal encephalocele can be challenging due to factors such as a difficult airway, associated systemic conditions, young age, and prolonged operating time. Hereby, we outline the intraoperative management of a 3-year-old child undergoing repair of multiple defects requiring multidisciplinary involvement of neurosurgery, plastic surgery, and anesthesia team. In our case, a size 0 mask and hyper-angulated D-blade video laryngoscopy were used to prevent sac compression and facilitate intubation. Blood conservation strategies included tranexamic acid, precise fluid management, and maintenance of normothermia. Extubation was carefully planned, considering blood loss and airway edema, and performed when the child was fully awake, ensuring a stable postoperative period and successful recovery. This report emphasizes the importance of meticulous preoperative assessment, readiness for a challenging airway, efficient management of intraoperative blood loss, and the value of teamwork.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1791955encephalocelemicrostomiaperioperative
spellingShingle Selvendiran Panneerselvam
Georgene Singh
Ananth P. Abraham
Keta Thakkar
Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
Journal of Neuroanaesthesiology and Critical Care
encephalocele
microstomia
perioperative
title Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
title_full Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
title_fullStr Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
title_full_unstemmed Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
title_short Anesthetic Management of a Child with Frontonasal Encephalocele and Hemifacial Microstomia Syndrome for Repair of Encephalocele and Microstomia Correction
title_sort anesthetic management of a child with frontonasal encephalocele and hemifacial microstomia syndrome for repair of encephalocele and microstomia correction
topic encephalocele
microstomia
perioperative
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0044-1791955
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