Adult onset sporadic ataxias: a diagnostic challenge
Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic cond...
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| Format: | Article |
| Language: | English |
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Thieme Revinter Publicações
2014-03-01
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| Series: | Arquivos de Neuro-Psiquiatria |
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| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232&lng=en&tlng=en |
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| _version_ | 1849686980790583296 |
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| author | Orlando Graziani Povoas Barsottini Marcus Vinicius Cristino de Albuquerque Pedro Braga Neto José Luiz Pedroso |
| author_facet | Orlando Graziani Povoas Barsottini Marcus Vinicius Cristino de Albuquerque Pedro Braga Neto José Luiz Pedroso |
| author_sort | Orlando Graziani Povoas Barsottini |
| collection | DOAJ |
| description | Patients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria. |
| format | Article |
| id | doaj-art-02061ae5c4bb49e381afc4ee4732b3d9 |
| institution | DOAJ |
| issn | 1678-4227 |
| language | English |
| publishDate | 2014-03-01 |
| publisher | Thieme Revinter Publicações |
| record_format | Article |
| series | Arquivos de Neuro-Psiquiatria |
| spelling | doaj-art-02061ae5c4bb49e381afc4ee4732b3d92025-08-20T03:22:29ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria1678-42272014-03-0172323224010.1590/0004-282X20130242S0004-282X2014000300232Adult onset sporadic ataxias: a diagnostic challengeOrlando Graziani Povoas BarsottiniMarcus Vinicius Cristino de AlbuquerquePedro Braga NetoJosé Luiz PedrosoPatients with adult onset non-familial progressive ataxia are classified in sporadic ataxia group. There are several disease categories that may manifest with sporadic ataxia: toxic causes, immune-mediated ataxias, vitamin deficiency, infectious diseases, degenerative disorders and even genetic conditions. Considering heterogeneity in the clinical spectrum of sporadic ataxias, the correct diagnosis remains a clinical challenge. In this review, the different disease categories that lead to sporadic ataxia with adult onset are discussed with special emphasis on their clinical and neuroimaging features, and diagnostic criteria.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232&lng=en&tlng=enataxiaataxias esporádicasaspectos clínicoscritérios diagnósticos |
| spellingShingle | Orlando Graziani Povoas Barsottini Marcus Vinicius Cristino de Albuquerque Pedro Braga Neto José Luiz Pedroso Adult onset sporadic ataxias: a diagnostic challenge Arquivos de Neuro-Psiquiatria ataxia ataxias esporádicas aspectos clínicos critérios diagnósticos |
| title | Adult onset sporadic ataxias: a diagnostic challenge |
| title_full | Adult onset sporadic ataxias: a diagnostic challenge |
| title_fullStr | Adult onset sporadic ataxias: a diagnostic challenge |
| title_full_unstemmed | Adult onset sporadic ataxias: a diagnostic challenge |
| title_short | Adult onset sporadic ataxias: a diagnostic challenge |
| title_sort | adult onset sporadic ataxias a diagnostic challenge |
| topic | ataxia ataxias esporádicas aspectos clínicos critérios diagnósticos |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2014000300232&lng=en&tlng=en |
| work_keys_str_mv | AT orlandograzianipovoasbarsottini adultonsetsporadicataxiasadiagnosticchallenge AT marcusviniciuscristinodealbuquerque adultonsetsporadicataxiasadiagnosticchallenge AT pedrobraganeto adultonsetsporadicataxiasadiagnosticchallenge AT joseluizpedroso adultonsetsporadicataxiasadiagnosticchallenge |