Absent pulmonary valve syndrome with agenesis of the left pulmonary artery
Absent pulmonary valve syndrome is represented by rudimentary nodules without identifiable leaflets, and it is commonly associated with a ventricular septal defect and tetralogy of Fallot. Unilateral absence of a pulmonary artery is also a rare congenital anomaly. The following is a case repo...
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| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Hacettepe University Institute of Child Health
1994-07-01
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| Series: | The Turkish Journal of Pediatrics |
| Online Access: | https://turkjpediatr.org/article/view/3634 |
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| _version_ | 1850033362352209920 |
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| author | A Paç S Ozme A Celiker S Ozkutlu |
| author_facet | A Paç S Ozme A Celiker S Ozkutlu |
| author_sort | A Paç |
| collection | DOAJ |
| description |
Absent pulmonary valve syndrome is represented by rudimentary nodules without identifiable leaflets, and it is commonly associated with a ventricular septal defect and tetralogy of Fallot. Unilateral absence of a pulmonary artery is also a rare congenital anomaly. The following is a case report of a one-day-old newborn with cyanosis. The physical examination revealed a to-and-fro murmur and no expansion of the left hemithorax. Echocardiography revealed tetralogy of Fallot, absent pulmonary valve, and enlarged main and right pulmonary arteries. The catheterization and angiography confirmed the diagnosis and absence of the left pulmonary artery.
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| format | Article |
| id | doaj-art-01cd77bb415d43dca66ed243499f53fe |
| institution | DOAJ |
| issn | 0041-4301 2791-6421 |
| language | English |
| publishDate | 1994-07-01 |
| publisher | Hacettepe University Institute of Child Health |
| record_format | Article |
| series | The Turkish Journal of Pediatrics |
| spelling | doaj-art-01cd77bb415d43dca66ed243499f53fe2025-08-20T02:58:15ZengHacettepe University Institute of Child HealthThe Turkish Journal of Pediatrics0041-43012791-64211994-07-01363Absent pulmonary valve syndrome with agenesis of the left pulmonary arteryA Paç0S OzmeA CelikerS OzkutluDepartment of Pediatrics, Hacettepe University Faculty of Medicine, Ankara. Absent pulmonary valve syndrome is represented by rudimentary nodules without identifiable leaflets, and it is commonly associated with a ventricular septal defect and tetralogy of Fallot. Unilateral absence of a pulmonary artery is also a rare congenital anomaly. The following is a case report of a one-day-old newborn with cyanosis. The physical examination revealed a to-and-fro murmur and no expansion of the left hemithorax. Echocardiography revealed tetralogy of Fallot, absent pulmonary valve, and enlarged main and right pulmonary arteries. The catheterization and angiography confirmed the diagnosis and absence of the left pulmonary artery. https://turkjpediatr.org/article/view/3634 |
| spellingShingle | A Paç S Ozme A Celiker S Ozkutlu Absent pulmonary valve syndrome with agenesis of the left pulmonary artery The Turkish Journal of Pediatrics |
| title | Absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| title_full | Absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| title_fullStr | Absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| title_full_unstemmed | Absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| title_short | Absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| title_sort | absent pulmonary valve syndrome with agenesis of the left pulmonary artery |
| url | https://turkjpediatr.org/article/view/3634 |
| work_keys_str_mv | AT apac absentpulmonaryvalvesyndromewithagenesisoftheleftpulmonaryartery AT sozme absentpulmonaryvalvesyndromewithagenesisoftheleftpulmonaryartery AT aceliker absentpulmonaryvalvesyndromewithagenesisoftheleftpulmonaryartery AT sozkutlu absentpulmonaryvalvesyndromewithagenesisoftheleftpulmonaryartery |