NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma

Anaplastic thyroid carcinoma (ATC) is among the most daunting entities in clinical oncology. Large-scale genomic studies of thyroid cancer within the last decade have uncovered a distinct set of recurrent somatic alterations implicated in the development, aggressiveness, and treatment resistance of...

Full description

Saved in:
Bibliographic Details
Main Authors: Amir Hossein Karimi, Peter YF Zeng, Matthew Cecchini, John W Barrett, Harrison Pan, Shengjie Ying, Nhi Le, Joe S Mymryk, Laurie E Ailles, Anthony C Nichols
Format: Article
Language:English
Published: Bioscientifica 2025-06-01
Series:European Thyroid Journal
Subjects:
Online Access:https://etj.bioscientifica.com/view/journals/etj/14/3/ETJ-25-0057.xml
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850231517029072896
author Amir Hossein Karimi
Peter YF Zeng
Matthew Cecchini
John W Barrett
Harrison Pan
Shengjie Ying
Nhi Le
Joe S Mymryk
Laurie E Ailles
Anthony C Nichols
author_facet Amir Hossein Karimi
Peter YF Zeng
Matthew Cecchini
John W Barrett
Harrison Pan
Shengjie Ying
Nhi Le
Joe S Mymryk
Laurie E Ailles
Anthony C Nichols
author_sort Amir Hossein Karimi
collection DOAJ
description Anaplastic thyroid carcinoma (ATC) is among the most daunting entities in clinical oncology. Large-scale genomic studies of thyroid cancer within the last decade have uncovered a distinct set of recurrent somatic alterations implicated in the development, aggressiveness, and treatment resistance of ATC. The sequence of events leading to the development of ATC commonly begins with a tumorigenic mutation that constitutively activates the mitogen-activated protein kinase (MAPK) pathway, giving rise to indolent entities such as well-differentiated papillary or follicular thyroid carcinomas. This is followed by recurring alterations that drive oncogenic properties such as enhanced proliferation, genomic instability, replicative immortality, and dedifferentiation, culminating in the emergence of highly aggressive ATC tumors. The truncal MAPK-activating events present therapeutic opportunities, as small molecule inhibitors against key components of this pathway are available. Indeed, genotype-guided targeting of the MAPK pathway is now the standard of care for subgroups of ATC patients, and further efforts exploring additional MAPK inhibitors and the combination of immune checkpoint blockade with MAPK inhibition are overcoming resistance to the current targeted therapies in the clinic and expanding our arsenal against this disease. In this review, we summarize the current understanding of the genomic landscape of ATC, discuss the biological and clinical ramifications of recurring aberrations, and provide an overview of the opportunities and challenges in the clinical management of this lethal malignancy.
format Article
id doaj-art-00f74e461172432ea02ddd595089a148
institution OA Journals
issn 2235-0802
language English
publishDate 2025-06-01
publisher Bioscientifica
record_format Article
series European Thyroid Journal
spelling doaj-art-00f74e461172432ea02ddd595089a1482025-08-20T02:03:31ZengBioscientificaEuropean Thyroid Journal2235-08022025-06-0114310.1530/ETJ-25-00571NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinomaAmir Hossein Karimi0Peter YF Zeng1Matthew Cecchini2John W Barrett3Harrison Pan4Shengjie Ying5Nhi Le6Joe S Mymryk7Laurie E Ailles8Anthony C Nichols9Department of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Pathology and Laboratory Medicine, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaPrincess Margaret Cancer Centre, University Health Network, Toronto, Ontario, CanadaDepartment of Otolaryngology – Head & Neck Surgery, Western University, London, Ontario, CanadaAnaplastic thyroid carcinoma (ATC) is among the most daunting entities in clinical oncology. Large-scale genomic studies of thyroid cancer within the last decade have uncovered a distinct set of recurrent somatic alterations implicated in the development, aggressiveness, and treatment resistance of ATC. The sequence of events leading to the development of ATC commonly begins with a tumorigenic mutation that constitutively activates the mitogen-activated protein kinase (MAPK) pathway, giving rise to indolent entities such as well-differentiated papillary or follicular thyroid carcinomas. This is followed by recurring alterations that drive oncogenic properties such as enhanced proliferation, genomic instability, replicative immortality, and dedifferentiation, culminating in the emergence of highly aggressive ATC tumors. The truncal MAPK-activating events present therapeutic opportunities, as small molecule inhibitors against key components of this pathway are available. Indeed, genotype-guided targeting of the MAPK pathway is now the standard of care for subgroups of ATC patients, and further efforts exploring additional MAPK inhibitors and the combination of immune checkpoint blockade with MAPK inhibition are overcoming resistance to the current targeted therapies in the clinic and expanding our arsenal against this disease. In this review, we summarize the current understanding of the genomic landscape of ATC, discuss the biological and clinical ramifications of recurring aberrations, and provide an overview of the opportunities and challenges in the clinical management of this lethal malignancy.https://etj.bioscientifica.com/view/journals/etj/14/3/ETJ-25-0057.xmlanaplastic thyroid carcinomagenomicstargeted therapyimmunotherapy
spellingShingle Amir Hossein Karimi
Peter YF Zeng
Matthew Cecchini
John W Barrett
Harrison Pan
Shengjie Ying
Nhi Le
Joe S Mymryk
Laurie E Ailles
Anthony C Nichols
NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
European Thyroid Journal
anaplastic thyroid carcinoma
genomics
targeted therapy
immunotherapy
title NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
title_full NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
title_fullStr NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
title_full_unstemmed NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
title_short NOVEL INSIGHTS IN ADVANCED THYROID CARCINOMA: FROM MECHANISMS TO TREATMENTS: Molecular insights into the origin, biology, and treatment of anaplastic thyroid carcinoma
title_sort novel insights in advanced thyroid carcinoma from mechanisms to treatments molecular insights into the origin biology and treatment of anaplastic thyroid carcinoma
topic anaplastic thyroid carcinoma
genomics
targeted therapy
immunotherapy
url https://etj.bioscientifica.com/view/journals/etj/14/3/ETJ-25-0057.xml
work_keys_str_mv AT amirhosseinkarimi novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT peteryfzeng novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT matthewcecchini novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT johnwbarrett novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT harrisonpan novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT shengjieying novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT nhile novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT joesmymryk novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT laurieeailles novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma
AT anthonycnichols novelinsightsinadvancedthyroidcarcinomafrommechanismstotreatmentsmolecularinsightsintotheoriginbiologyandtreatmentofanaplasticthyroidcarcinoma