Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans
ABSTRACT This case outlines the stepwise evaluation of a growing plaque on the back of a 6‐year‐old boy mimicking dermatofibrosarcoma protuberans. Further investigations, including echography and two biopsies, led to the unexpected diagnosis of Localised Chronic Fibrosing Vasculitis, highlighting th...
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| Format: | Article |
| Language: | English |
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Wiley
2025-06-01
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| Series: | JEADV Clinical Practice |
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| Online Access: | https://doi.org/10.1002/jvc2.595 |
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| author | Michela Brena Italo Francesco Aromolo Nicola Adriano Monzani Stefano Cambiaghi Giorgio Alberto Croci Chiara Benaglia Riccardo Cavalli |
| author_facet | Michela Brena Italo Francesco Aromolo Nicola Adriano Monzani Stefano Cambiaghi Giorgio Alberto Croci Chiara Benaglia Riccardo Cavalli |
| author_sort | Michela Brena |
| collection | DOAJ |
| description | ABSTRACT This case outlines the stepwise evaluation of a growing plaque on the back of a 6‐year‐old boy mimicking dermatofibrosarcoma protuberans. Further investigations, including echography and two biopsies, led to the unexpected diagnosis of Localised Chronic Fibrosing Vasculitis, highlighting the importance of considering rare entities in challenging cases. |
| format | Article |
| id | doaj-art-e419bba3f25e41e4b05f256bc72dc247 |
| institution | DOAJ |
| issn | 2768-6566 |
| language | English |
| publishDate | 2025-06-01 |
| publisher | Wiley |
| record_format | Article |
| series | JEADV Clinical Practice |
| spelling | doaj-art-e419bba3f25e41e4b05f256bc72dc2472025-08-20T03:06:53ZengWileyJEADV Clinical Practice2768-65662025-06-014251952110.1002/jvc2.595Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma ProtuberansMichela Brena0Italo Francesco Aromolo1Nicola Adriano Monzani2Stefano Cambiaghi3Giorgio Alberto Croci4Chiara Benaglia5Riccardo Cavalli6Department of Clinical Sciences and Community Health Pediatric Dermatology Unit, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico Milan ItalyDepartment of Pathophysiology and Transplantation University of Milan Milan ItalyDepartment of Clinical Science and Community Health University of Milan Milan ItalyDepartment of Clinical Sciences and Community Health Pediatric Dermatology Unit, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico Milan ItalyDepartment of Pathophysiology and Transplantation University of Milan Milan ItalyDepartment of Pathophysiology and Transplantation University of Milan Milan ItalyDepartment of Clinical Sciences and Community Health Pediatric Dermatology Unit, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico Milan ItalyABSTRACT This case outlines the stepwise evaluation of a growing plaque on the back of a 6‐year‐old boy mimicking dermatofibrosarcoma protuberans. Further investigations, including echography and two biopsies, led to the unexpected diagnosis of Localised Chronic Fibrosing Vasculitis, highlighting the importance of considering rare entities in challenging cases.https://doi.org/10.1002/jvc2.595IgG4inflammatory skin diseasespaediatric dermatologyvasculitis |
| spellingShingle | Michela Brena Italo Francesco Aromolo Nicola Adriano Monzani Stefano Cambiaghi Giorgio Alberto Croci Chiara Benaglia Riccardo Cavalli Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans JEADV Clinical Practice IgG4 inflammatory skin diseases paediatric dermatology vasculitis |
| title | Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans |
| title_full | Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans |
| title_fullStr | Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans |
| title_full_unstemmed | Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans |
| title_short | Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans |
| title_sort | localised chronic fibrosing vasculitis in a 6 year old boy clinically mimicking dermatofibrosarcoma protuberans |
| topic | IgG4 inflammatory skin diseases paediatric dermatology vasculitis |
| url | https://doi.org/10.1002/jvc2.595 |
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