Engine breakdown of lysosomes and related organelles and the resulting physiology

Late endosomes/lysosomes (LE/Lys) and lysosome related organelles (LROs) move dynamically through cells which involves many levels of regulation. To reach their destination, they need to connect to the motor proteins dynein-dynactin, kinesin or myosin for long-range bidirectional transport along mic...

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Main Authors: Nina Bakker, Marlieke L. M. Jongsma, Jacques Neefjes
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-06-01
Series:Frontiers in Cell and Developmental Biology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fcell.2025.1575571/full
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author Nina Bakker
Marlieke L. M. Jongsma
Jacques Neefjes
author_facet Nina Bakker
Marlieke L. M. Jongsma
Jacques Neefjes
author_sort Nina Bakker
collection DOAJ
description Late endosomes/lysosomes (LE/Lys) and lysosome related organelles (LROs) move dynamically through cells which involves many levels of regulation. To reach their destination, they need to connect to the motor proteins dynein-dynactin, kinesin or myosin for long-range bidirectional transport along microtubules and short-range movement along actin filaments. This connection depends on various factors at the microtubule, including the MAP- and tubulin-code, as well as adaptors, Rab GTPases and effector proteins marking the LE/Lys and LRO membranes. Mutations affecting this transport results in defective LE/Lys or LRO cargo delivery often resulting in skin, neurological and/or immunological diseases. How LE/Lys and LRO transport is orchestrated and how it fails in disease states, will be discussed.
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publisher Frontiers Media S.A.
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series Frontiers in Cell and Developmental Biology
spelling doaj-art-8f4ec2624c1a436789a9676cb15885c92025-08-20T03:20:14ZengFrontiers Media S.A.Frontiers in Cell and Developmental Biology2296-634X2025-06-011310.3389/fcell.2025.15755711575571Engine breakdown of lysosomes and related organelles and the resulting physiologyNina BakkerMarlieke L. M. JongsmaJacques NeefjesLate endosomes/lysosomes (LE/Lys) and lysosome related organelles (LROs) move dynamically through cells which involves many levels of regulation. To reach their destination, they need to connect to the motor proteins dynein-dynactin, kinesin or myosin for long-range bidirectional transport along microtubules and short-range movement along actin filaments. This connection depends on various factors at the microtubule, including the MAP- and tubulin-code, as well as adaptors, Rab GTPases and effector proteins marking the LE/Lys and LRO membranes. Mutations affecting this transport results in defective LE/Lys or LRO cargo delivery often resulting in skin, neurological and/or immunological diseases. How LE/Lys and LRO transport is orchestrated and how it fails in disease states, will be discussed.https://www.frontiersin.org/articles/10.3389/fcell.2025.1575571/fulllysosomeslysosome-related organelles (LROs)transportkinesindyneinmicrotubules
spellingShingle Nina Bakker
Marlieke L. M. Jongsma
Jacques Neefjes
Engine breakdown of lysosomes and related organelles and the resulting physiology
Frontiers in Cell and Developmental Biology
lysosomes
lysosome-related organelles (LROs)
transport
kinesin
dynein
microtubules
title Engine breakdown of lysosomes and related organelles and the resulting physiology
title_full Engine breakdown of lysosomes and related organelles and the resulting physiology
title_fullStr Engine breakdown of lysosomes and related organelles and the resulting physiology
title_full_unstemmed Engine breakdown of lysosomes and related organelles and the resulting physiology
title_short Engine breakdown of lysosomes and related organelles and the resulting physiology
title_sort engine breakdown of lysosomes and related organelles and the resulting physiology
topic lysosomes
lysosome-related organelles (LROs)
transport
kinesin
dynein
microtubules
url https://www.frontiersin.org/articles/10.3389/fcell.2025.1575571/full
work_keys_str_mv AT ninabakker enginebreakdownoflysosomesandrelatedorganellesandtheresultingphysiology
AT marliekelmjongsma enginebreakdownoflysosomesandrelatedorganellesandtheresultingphysiology
AT jacquesneefjes enginebreakdownoflysosomesandrelatedorganellesandtheresultingphysiology