Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis

Pulmonary agenesis (PA) is a rare developmental malformation, with a frequency of approximately 1 in 10–15,000 pregnancies. Unilateral PA is often associated with other congenital anomalies, whereas bilateral PA is fatal. Prenatal diagnosis is rare and is diagnosed more frequently in the postnatal p...

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Main Authors: Eduardo Reyna-Villasmil, Liliana Briceño-Sanabria, Juan Carlos Briceño-Sanabria, Carlos Briceño-Pérez
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-08-01
Series:Journal of Medical Ultrasound
Subjects:
Online Access:https://journals.lww.com/10.4103/jmu.jmu_24_23
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author Eduardo Reyna-Villasmil
Liliana Briceño-Sanabria
Juan Carlos Briceño-Sanabria
Carlos Briceño-Pérez
author_facet Eduardo Reyna-Villasmil
Liliana Briceño-Sanabria
Juan Carlos Briceño-Sanabria
Carlos Briceño-Pérez
author_sort Eduardo Reyna-Villasmil
collection DOAJ
description Pulmonary agenesis (PA) is a rare developmental malformation, with a frequency of approximately 1 in 10–15,000 pregnancies. Unilateral PA is often associated with other congenital anomalies, whereas bilateral PA is fatal. Prenatal diagnosis is rare and is diagnosed more frequently in the postnatal period than in the prenatal period. Is a challenge that may be difficult as it shares similar features with other more common pathologies. Ultrasound plays a crucial role in early diagnosis and management. Ultrasonographic findings for a correct prenatal diagnosis include mediastinum displacement with the absence of parenchymal or cystic tissue, decreased thoracic volume, an elevated diaphragm, cardiac axis deviation, and a hemithoracic cavity largely occupied by the heart. Cases of right PA have a worse prognosis compared to left PA, probably due to higher frequency of cardiac and great vessel abnormalities. A rare case of early prenatal ultrasound diagnosis of unilateral fetal PA, at 18 weeks of gestation, is reported.
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issn 0929-6441
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language English
publishDate 2024-08-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Journal of Medical Ultrasound
spelling doaj-art-8f458362e51b4dd7a873f3d09a7ef5ca2025-08-20T02:09:45ZengWolters Kluwer Medknow PublicationsJournal of Medical Ultrasound0929-64412212-15522024-08-0132325926110.4103/jmu.jmu_24_23Prenatal Ultrasound Diagnosis of Unilateral Pulmonary AgenesisEduardo Reyna-VillasmilLiliana Briceño-SanabriaJuan Carlos Briceño-SanabriaCarlos Briceño-PérezPulmonary agenesis (PA) is a rare developmental malformation, with a frequency of approximately 1 in 10–15,000 pregnancies. Unilateral PA is often associated with other congenital anomalies, whereas bilateral PA is fatal. Prenatal diagnosis is rare and is diagnosed more frequently in the postnatal period than in the prenatal period. Is a challenge that may be difficult as it shares similar features with other more common pathologies. Ultrasound plays a crucial role in early diagnosis and management. Ultrasonographic findings for a correct prenatal diagnosis include mediastinum displacement with the absence of parenchymal or cystic tissue, decreased thoracic volume, an elevated diaphragm, cardiac axis deviation, and a hemithoracic cavity largely occupied by the heart. Cases of right PA have a worse prognosis compared to left PA, probably due to higher frequency of cardiac and great vessel abnormalities. A rare case of early prenatal ultrasound diagnosis of unilateral fetal PA, at 18 weeks of gestation, is reported.https://journals.lww.com/10.4103/jmu.jmu_24_23fetal pulmonary malformationslung agenesisprenatal diagnosispulmonary agenesis
spellingShingle Eduardo Reyna-Villasmil
Liliana Briceño-Sanabria
Juan Carlos Briceño-Sanabria
Carlos Briceño-Pérez
Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
Journal of Medical Ultrasound
fetal pulmonary malformations
lung agenesis
prenatal diagnosis
pulmonary agenesis
title Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
title_full Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
title_fullStr Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
title_full_unstemmed Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
title_short Prenatal Ultrasound Diagnosis of Unilateral Pulmonary Agenesis
title_sort prenatal ultrasound diagnosis of unilateral pulmonary agenesis
topic fetal pulmonary malformations
lung agenesis
prenatal diagnosis
pulmonary agenesis
url https://journals.lww.com/10.4103/jmu.jmu_24_23
work_keys_str_mv AT eduardoreynavillasmil prenatalultrasounddiagnosisofunilateralpulmonaryagenesis
AT lilianabricenosanabria prenatalultrasounddiagnosisofunilateralpulmonaryagenesis
AT juancarlosbricenosanabria prenatalultrasounddiagnosisofunilateralpulmonaryagenesis
AT carlosbricenoperez prenatalultrasounddiagnosisofunilateralpulmonaryagenesis