An Ultra-Rare Disorder: Case Report on Cerebrotendinous Xanthomatosis

<b>Background and Clinical Significance:</b> Cerebrotendinous xanthomatosis (CTX) is a rare autosomal recessive disorder caused by mutations in the <i>CYP27A1</i> gene, leading to impaired bile acid synthesis and systemic cholesterol deposition. The condition presents with a...

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Bibliographic Details
Main Authors: Mariya Levkova, Mari Hachmeriyan, Margarita Grudkova, Mihael Tsalta-Mladenov, Ara Kaprelyan
Format: Article
Language:English
Published: MDPI AG 2025-05-01
Series:Reports
Subjects:
Online Access:https://www.mdpi.com/2571-841X/8/2/77
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